Pleuropulmonary manifestations of amyloidosis - UpToDate
Amyloidosis results from the misfolding and orderly aggregation of proteins into fibrils that are deposited in tissues resulting in disruption of function of major organs. Over 30 proteins have been described to be amyloidogenic in humans, but …
Pulmonary amyloidosis | Radiology Reference Article ...
2021年10月21日 · Pulmonary amyloidosis is a rare manifestation of amyloidosis characterized by involvement of lung parenchyma. Two patterns are described: nodular parenchymal amyloidosis (more common) diffuse parenchymal amyloidosis (least common type)
Pulmonary manifestations of amyloidosis - Respiratory Medicine
2023年6月13日 · Amyloidosis is a rare but pervasive disease and can involve different regions of the lung including airways, lung parenchyma and pleura. We describe four patterns of pulmonary involvement in amyloidosis.
Pulmonary AL amyloidosis: A review and update on treatment ...
Pulmonary amyloidosis is frequently characterized by the AL amyloid subtype and can be localized or associated with systemic involvement, presenting in a nodular, diffuse alveolar-septal, or tracheobronchial pattern. Presentation of disease can vary from clinically silent to severe.
The lung in amyloidosis - PMC - PubMed Central (PMC)
Amyloidosis is a disorder caused by misfolding of autologous protein and its extracellular deposition as fibrils, resulting in vital organ dysfunction and eventually death. Pulmonary amyloidosis may be localised or part of systemic amyloidosis.
Pulmonary amyloidosis - EMCrit Project
2024年3月10日 · Amyloidosis is a disorder that involves the deposition of protein conglomerates in the extracellular tissue. Different types of amyloidosis result from the deposition of different types of protein. A common type is AL amyloidosis, which results from plasma cells' overproduction of light chain proteins. systemic vs. localized AL amyloidosis
The spectrum of pulmonary amyloidosis - Respiratory Medicine
2023年5月7日 · Amyloidosis is a disease caused by misfolded proteins that deposit in the extracellular matrix as fibrils, resulting in the dysfunction of the involved organ. The lung is a common target of Amyloidosis, but pulmonary amyloidosis is uncommonly diagnosed since it is rarely symptomatic.